Cell Lines SCA3 CENSOi071-A Cell type hiPSC Causal gene(s) ATXN3 Mutation 75/14 CAG RRID CVCL_E4G3 Originating lab Censo and Axol Bioscience Company (CENSO) View details →
Cell Lines SCA3 ChHES-472 Cell type hESC Causal gene(s) ATXN3 Mutation 74 CAG RRID CVCL_XA13 Originating lab National Engineering and Research Center of Human Stem Cell View details →
Cell Lines SCA2 CHOPi002-A Cell type hiPSC Causal gene(s) ATXN2 Mutation 23/33 CAG RRID CVCL_UL69 Originating lab The Children's Hospital of Philadelphia (CHOP) View details →
Cell Lines SCA2 CHOPi003-A Cell type hiPSC Causal gene(s) ATXN2 Mutation 23/43 CAG RRID CVCL_UL70 Originating lab The Children's Hospital of Philadelphia (CHOP) View details →
Cell Lines SACS/ARSACS/SPAX6 CHUQi002-A Cell type hiPSC Causal gene(s) SACS Mutation 0c.9497-9498delTT RRID CVCL_E3RD Originating lab CRCHU de Quebec's induced pluripotency stem cells production platform View details →
Cell Lines SACS/ARSACS/SPAX6 CHUQi003-A Cell type hiPSC Causal gene(s) SACS Originating lab CHU de Quebec-Universite Laval Research Center (CHUQ) View details →
Cell Lines SACS/ARSACS/SPAX6 CHUQi004-A Cell type hiPSC Causal gene(s) SACS Mutation 0c.6594delT/c.7504C>T Originating lab CRCHU de Quebec's induced pluripotency stem cells production platform View details →
Cell Lines SACS/ARSACS/SPAX6 CHUQi005-A Cell type hiPSC Causal gene(s) SACS Mutation 0c.4205A>T/c.5836 T>C Originating lab CRCHU de Quebec's induced pluripotency stem cells production platform View details →
Cell Lines SACS/ARSACS/SPAX6 CHUQi006-A Cell type hiPSC Causal gene(s) SACS Mutation 0c.6594delT Originating lab CRCHU de Quebec's induced pluripotency stem cells production platform View details →
Cell Lines SACS/ARSACS/SPAX6 CHUQi007-A Cell type hiPSC Causal gene(s) SACS Mutation 0c.6594delT Originating lab CRCHU de Quebec's induced pluripotency stem cells production platform View details →
Cell Lines SACS/ARSACS/SPAX6 CHUQi008-A Cell type hiPSC Causal gene(s) SACS Mutation 0c.6594delT Originating lab CRCHU de Quebec's induced pluripotency stem cells production platform View details →
Cell Lines SACS/ARSACS/SPAX6 CHUQi009-A Cell type hiPSC Causal gene(s) SACS Mutation 0c.6594delT Originating lab CRCHU de Quebec's induced pluripotency stem cells production platform View details →
Cell Lines SACS/ARSACS/SPAX6 CHUQi010-A Cell type hiPSC Causal gene(s) SACS Mutation 0c.6594delT Originating lab CRCHU de Quebec's induced pluripotency stem cells production platform View details →
Cell Lines SCA1 CJUHi001 Cell type hiPSC Causal gene(s) ATXN1 Mutation ?/44 CAG RRID CVCL_C6TW Originating lab China-Japan Union Hospital of Jilin University (CJUH) View details →
Mouse Models MSA/OPCA CNP-SNCAGFP Tg mice Model type Transgenic Mouse strain C57BL6/J Causal gene(s) Sporadic Mutation expressing human αsyn-green fluorescent protein (GFP) fusion proteins in oligodendrocytes Originating lab Kyoto University View details →
Mouse Models MSA/OPCA CNP-α-syn transgenic mouse Model type Transgenic Causal gene(s) Sporadic Mutation Expression of wild-type human α-syn and P301L mutant tau (tauP301L) Originating lab University of Pennsylvania School of Medicine View details →
Mouse Models SCA11 conditional Ttbk2 KO (Ttbk2c.mut) Model type Knockout Causal gene(s) TTBK2 Mutation Ubiquitous conditional Ttbk2 knockout Originating lab Duke University View details →
Mouse Models SCA11 conditional Ttbk2 KO (Ttbk2pcp2) Model type Knockout Causal gene(s) TTBK2 Mutation Conditional Ttbk2 knockout specifically in the Purkinje cells Originating lab Duke University View details →
Mouse Models SCA11 conditional Ttbk2 KO (Ttbk2slc1a3) Model type Knockout Causal gene(s) TTBK2 Mutation Conditional Ttbk2 knockout specifically in the Bergmann glia Originating lab Duke University View details →
Cell Lines SCA3 Corrected iPSC (C-iPSC) Cell type hiPSC Causal gene(s) ATXN3 Mutation 26/- CAG (ΔpolyQ) Originating lab Third affiliated Hospital of Guangzhou Medical University View details →